By Disease Name > Klippel-Trenauny-weber syndrome

Nevus Flammeus

Top  Previous  Next
•AKA “port-wine stain”
•AKA “salmon patch” – when located at nape of neck

 

Sturge-Weber syndrome

•AKA encephalotrigeminal angiomatosis
•sporadic
•facial port wine stain; ipsilateral glaucoma
•ipsilateral leptomeningeal vascular malformation
•atrophy and tram track calcification of underlying cerebral cortex
•seizures, mental retardation (50%)

Klippel-Trenauny-weber syndrome

•AKA osteohypertrophic nevus flammeus
•sporadic
•capillary malformation involving lower extremity; unilateral
•increased vascular supply causes limb hypertrophy
•ddx: for limb hypertrophy  Proteus syndrome; Maffucci syndrome