| • | AKA “salmon patch” – when located at nape of neck |
Sturge-Weber syndrome
| • | AKA encephalotrigeminal angiomatosis |
| • | facial port wine stain; ipsilateral glaucoma |
| • | ipsilateral leptomeningeal vascular malformation |
| • | atrophy and tram track calcification of underlying cerebral cortex |
| • | seizures, mental retardation (50%) |
Klippel-Trenauny-weber syndrome
| • | AKA osteohypertrophic nevus flammeus |
| • | capillary malformation involving lower extremity; unilateral |
| • | increased vascular supply causes limb hypertrophy |
| • | ddx: for limb hypertrophy Proteus syndrome; Maffucci syndrome |
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