• | AKA “salmon patch” – when located at nape of neck |
Sturge-Weber syndrome
• | AKA encephalotrigeminal angiomatosis |
• | facial port wine stain; ipsilateral glaucoma |
• | ipsilateral leptomeningeal vascular malformation |
• | atrophy and tram track calcification of underlying cerebral cortex |
• | seizures, mental retardation (50%) |
Klippel-Trenauny-weber syndrome
• | AKA osteohypertrophic nevus flammeus |
• | capillary malformation involving lower extremity; unilateral |
• | increased vascular supply causes limb hypertrophy |
• | ddx: for limb hypertrophy Proteus syndrome; Maffucci syndrome |
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