| • | AKA hereditary osteoonychodysplasia (HOOD) |
| • | triangular lunula = pathognomonic |
| • | uncommon, autosomal dominant |
| • | interesting because involves abnormalities of ectodermal and mesodermal structure |
| ◆ | in every case, the thumb nails are always involved and the most affected and the remaining nails, if involved, are progressively less damaged from index to little finger (hypoplastic nails) |
| • | bilateral posterior iliac horns (another feature) |
| • | Lester iris; absent patella |
| • | mnemonic – these horns look like triangles and so do the lunula |
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