| • | mnemonic = FP and OEF (familial polyposis and jaw osteomas, epidermoid cysts, fibromas) |  
 | • | ~ 100% malignant adenocarcinoma by age 30,  therefore prophylactic colectomy |  
 | • | CHRPE (congenital hypertrophy of retinal pigment epithelium) = best marker for the disease |  
 | • | mnemonic - while Gardening you may hear birds CHRPing |  
  
 |