| • | AKA oral epithelial nevus |
| • | rare autosomal dominant disorder |
| • | the buccal mucosa is always involved |
differential diagnosis:
| • | leukoedema (is non-hereditary, is patchy rather than diffuse, and the white spongy changes to the mucosa disappear upon stretching) |
| • | pachyonychia congenita and dyskeratosis congenita – have a later onset and are associated with hair and nail changes |
| • | oral focal epithelial hyperplasia |
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