By Disease Name > Lichen Myxedematosus

Lichen Myxedematosus

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•AKA papular mucinosis
•pathogenesis unknown

 

characterized by:

 

1.a papular lichenoid eruption
•dome-shaped papules
•lesions may be densely grouped in a lichenoid fashion or may show a linear arrangement
•dorsa of the hands and fingers, the axillary folds, and the external surface of the arms and legs
•coalescence of the papules on the face, particularly in the glabella area, results in longitudinal folding, giving the appearance of leonine facies
•ddx: (other deposition diseases) lichen amyloid, colloid milium (? juxtaclavicular beaded lines, hamartoma moniliformis??)

 

2.paraproteinemia
•usually an IgG with lambda light chains
•is not a plasma cell dyscrasia
•no association with multiple myeloma (paraprotein of multiple myeloma is usually a monoclonal IgG with kappa light chains)
•mnemonic = PML (papular mucinosis with lambda light chains)

 

3.mucin in the dermis

 

 

•scleromyxedema: a clinical variant of papular mucinosis in which the disease is more generalized and is accompanied by erythema and sclerosis